April 11, 2011 (Monday) -Behcet's Disease
Today we had a diagnosis which was new to me....
Behçet's disease (Behçet's syndrome, Adamantiades’ syndrome, or "silk road disease") is a rare, systemic, form of vasculitis that often presents with mucous membrane ulceration, and ocular problems.
As a systemic disease, it also involves visceral organs such as the gastrointestinal tract, pulmonary, musculoskeletal, and neurological systems.
This syndrome can be fatal; death can be caused by complicated rupture of the vascular aneurysms, or severe neurological complications, and therefore immediate medical treatment is necessary.
The syndrome is rare In the UK, it is estimated to have about 1 case for every 100,000 people, but is common in the Middle East and
Asia, suggesting a possible cause endemic to the tropical areas.
It is not associated with cancer, and links with tissue-types are not certain but are under investigation.
It also does not follow the usual pattern for autoimmune diseases. However, one study has revealed a possible connection to food allergies, particularly to dairy products.
One lives and learns….
Labels: case study